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long-chain acyl-coa dehydrogenase deficiency

Medical Definition

A genetic disorder characterized by deficiency of the enzyme long-chain acyl-coenzyme a dehydrogenase that metabolizes long-chain fatty acids. signs and symptoms appear in infancy or childhood and may be triggered during fasting, illness or exercise. they include hypoglycemia, muscle weakness and lethargy.
Related Codes (1)
Code
Description
Billable
Details
E71.310Long chain/very long chain acyl CoA dehydrogenase deficiency

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