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juvenile myelomonocytic leukemia

Medical Definition

Juvenile myelomonocytic leukemia (jmml) is a lethal myeloproliferative disease of young childhood characterized clinically by overproduction of myelomonocytic cells and by the in vitro phenotype of hematopoietic progenitor hypersensitivity to granulocyte-macrophage colony-stimulating factor. [https://orcid.org/0000-0002-0736-9199, pmid:18954903]

Wikipedia Summary

Juvenile myelomonocytic leukemia (JMML) is a rare form of chronic leukemia (cancer of the blood) that affects children, commonly those aged four and younger. The name JMML now encompasses all diagnoses formerly referred to as juvenile chronic myeloid leukemia (JCML), chronic myelomonocytic leukemia of infancy, and infantile monosomy 7 syndrome...
Related Codes (4)
Code
Description
Billable
Details
C93.3Juvenile myelomonocytic leukemia
C93.30Juvenile myelomonocytic leukemia, not having achieved remission
C93.31Juvenile myelomonocytic leukemia, in remission
C93.32Juvenile myelomonocytic leukemia, in relapse

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