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E71

Disorders of branched-chain amino-acid metabolism and fatty-acid metabolism

Children (23)
Code
Description
Billable
Details
E71.0Maple-syrup-urine disease
E71.1Other disorders of branched-chain amino-acid metabolism
E71.11Branched-chain organic acidurias
E71.12Disorders of propionate metabolism
E71.19Other disorders of branched-chain amino-acid metabolism
E71.2Disorder of branched-chain amino-acid metabolism, unspecified
E71.3Disorders of fatty-acid metabolism
Type 1 Excludes (3)Type 2 Excludes (1)
E71.30Disorder of fatty-acid metabolism, unspecified
E71.31Disorders of fatty-acid oxidation
E71.32Disorders of ketone metabolism

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